Principles of Diagnosis and Treatment of Pheochromocytoma and Retroperitoneal Paraganglioma
摘要
Pheochromocytoma and retroperitoneal paraganglioma (PPGL) are neuroendocrine tumors derived from the neural crest cells of sympathetic and parasympathetic chain, including PPGL located in the adrenal medulla (85–90%) and PPGL located outside the adrenal gland (10–15%), the most common parts of which are located along with the abdominal aorta, bladder, chest, head, neck, and so on (Fig. 1.1). PPGL accounts for about 0.2–0.6% of hypertensive patients, with an annual incidence of about 0.8/100,000.