During a postnatal examination, an 11-day-old full-term male infant was diagnosed to have a heart murmur. Upon echocardiographic evaluation, it was discovered that he had aortic valve stenosis, showing a transvalvular flow velocity of 5.62 m/s and a pressure gradient of 75 mm Hg, coupled with an atrial septal defect (type II). Given the critical nature of the aortic valve stenosis and the presence of heart failure, early intervention was deemed crucial. Percutaneous balloon aortic valvuloplasty emerged as a viable treatment option for congenital aortic valve stenosis in children, offering the benefit of avoiding invasive open-heart surgery in neonates. The anesthetic management for this procedure was centered on maintaining cardiac output and coronary perfusion to ensure a successful surgical outcome.