A 10-year-old girl, who was diagnosed with tricuspid atresia (TA) due to cyanosis after birth, had undergone superior vena cava-pulmonary artery anastomosis surgery 7 years ago. She is now scheduled to undergo Fontan surgery under general anesthesia. After the initial surgery, the ventricular function of children with TA was partially preserved, but eventually, the Fontan surgery needs to be performed to bypass the obstructed tricuspid valve and right ventricle and introduce the venous blood completely into the pulmonary artery to establish the Fontan circulation. In addition to assessing the condition of the child after palliative surgery, both ventricular function and pulmonary blood flow are key points of concern for anesthesia during Fontan surgery.