Sturge Weber Syndrome: Search for the Stain

Sturge–Weber Syndrome (SWS) or encephalotrigeminal angiomatosis is a rare congenital disorder that affects the brain, skin, and eyes. It occurs sporadically with an incidence ranging from 1 in 20,000 to 50,000 live births without any race or gender predilection. In this case report, we would like to report a unique case of SWS where the patient presented with unilateral advanced glaucoma but in the absence of a port-wine stain on the eyelid.