Management of Patients with Asplenia and Immunodeficiency
摘要
Heterotaxy syndrome is a rare disorder with multiorgan involvement characterized by congenital heart defects and abnormal visceral arrangement of the chest and abdominal organs. It has two forms (although there is still an ongoing scientific/terminological debate as to if patients with mirage image arrangement of thoracoabdominal organs (situs inversus), representing a departure from the usual arrangement (situs solitus) should be included in heterotaxy syndrome group or not):