Mucinous cystic neoplasms (MCNs) of the liver are extremely rare and account for less than 5% of all liver cysts. MCNs consist of lesions previously designated as biliary cystadenomas (BCAs) and biliary cystadenocarcinomas (BCACs). Often found incidentally, MCNs are usually benign, slow-growing lesions. A small subset of patients may harbor an MCN with malignant potential. In turn, surgical resection is the recommended treatment option for most patients with MCN.