Apert syndrome is a complex congenital disorder characterized by craniofaciosynostosis, exorbitism, midface retrusion followed by multilevel airway obstruction, and syndactyly of upper and lower limbs. Management of this condition requires a multidisciplinary approach starting in early infancy, with surgical goals focused on alleviating intracranial pressure, protecting the ocular globe, improving airway function, and enhancing facial and limb aesthetics. Monobloc facial bipartition with distraction osteogenesis (MFBDO) has emerged as a superior technique not only for addressing midface retrusion but also for hypertelorism-associated vertical orbital dystopia, divergent strabismus in addition to soft tissue features being the down slanting of the palpebral fissure one of the most important in patients with Apert syndrome. Although MFBDO is effective and offers significant benefits, it is not widely performed in craniofacial centers worldwide. Although MFBDO presents advantages such as improved aesthetic outcomes and functional corrections, complications such as infection and cerebrospinal fluid (CSF) fistulae can occur. The choice between internal and external distractors remains debatable, with each offering distinct benefits. Further research and refinement of techniques are necessary to enhance the treatment outcomes in patients with Apert syndrome.