Ear, nose, and throat involvement often occurs in rheumatologic diseases and provides important clues for diagnosis. These findings may be the first symptom of a rheumatologic disease or may arise during the illness. Ear, nose, and throat issues can sometimes be overlooked because they may appear alone in the early stages of rheumatologic conditions. However, these findings are crucial for early diagnosis and can influence prognosis. The rheumatologic diseases that lead to ear, nose, and throat involvement primarily include rheumatoid arthritis, Sjögren’s syndrome, systemic lupus erythematosus, systemic sclerosis, and Behçet’s disease. Disease, Wegener granulomatosis (granulomatous polyangiitis), Churg-Strauss syndrome (eosinophilic granulomatous polyangiitis), Cogan syndrome, sarcoidosis, and relapsing polychondritis. In rheumatologic diseases, signs and symptoms such as bilateral parotid swelling, inflammation-related destruction of the auricle and nasal cartilage, chronic sinusitis, vertigo, sensorineural hearing loss, recurrent oral ulcers, spontaneous septal and palatal perforation, difficulty swallowing, and hoarseness may be observed.