Cardiac MRI in Restrictive Cardiomyopathy and Cardiac Amyloidosis
摘要
Restrictive cardiomyopathy (RCM) is a myocardial disorder that results from increased myocardial stiffness and impaired ventricular filling. It is usually associated with normal or near normal biventricular chamber size and systolic function until later stages of the disease. Cardiac magnetic resonance (CMR) is widely accepted as the non-invasive gold standard for visualizing and quantifying cardiovascular anatomy, biventricular volumes, myocardial mass, and regional/global systolic function and class I indication for specific cardiomyopathies, including Cardiac amyloidosis (CA). CMR has the strength of myocardial tissue characterization. In this chapter, we will discuss cases of cardiac amyloidosis, sarcoidosis, and Fabry disease with typical CMR findings.