Darier’s disease (DD) is an uncommon autosomal dominantly inherited acantholytic genodermatosis clinically showing discrete, greasy, hyperkeratotic, skin-colored, reddish-brown, or yellowish-brown papules which may sometimes coalesce into crusted plaques; seborrheic areas and skin creases are the main involved sites. DD displays a complex pattern characterized by polygonal, starlike, or roundish-oval-shaped yellowish/brownish structures, surrounded by a more or less thin whitish halo, on a pinkish homogeneous structureless area, with or without the presence of whitish scales and dotted and/or linear vessels.