Optic pits are colobomatous defects of the optic nerve usually presenting as hypopigmented lesions located in the inferotemporal part of the disc. They are usually seen as unilateral congenital anomaly; but rarely may be associated with glaucoma and myopia. Men and women are equally affected, with an incidence of 1/10,000. Most cases are asymptomatic, but some patients develop vision loss due to serous macular detachment. While a moderate decline in visual acuity is typically observed in the early period after serous macular detachment development, untreated, chronic cases may develop intraretinal cystoid degeneration, lamellar or full-thickness macular hole, and permanent severe (<20/200) visual impairment due to retinal pigment epithelium atrophy in the chronic course. A large optic pit may also cause an enlarged blind spot and paracentral arcuate scotoma.