This chapter discusses the presentations and management of retinal tumors. Retinal tumors can be classified clinically into melanotic, vascular, amelanotic, and calcified tumors. Melanotic retinal tumors include the lesions and tumors of the retinal pigment epithelium and metastatic cutaneous melanoma to the retina. Retinal vascular tumors and their associated syndromes are discussed. Amelanotic retinal tumors, including vitreoretinal lymphoma, retinal metastasis, and retinal gliotic tumors, are demonstrated. Retinal calcified tumors include retinal astrocytic hamartoma and retinoblastoma. Retinoblastoma, the most common pediatric intraocular tumor, is highlighted. Current information on retinoblastoma epidemiology, genetics, and inheritance is explained. The clinical presentations, differential diagnosis, imaging findings, grouping and staging, and the multiple systemic and regional treatment modalities of retinoblastoma are described in detail.