Dermatofibrosarcoma protuberansDermatofibrosarcoma protuberans (DFSP) is a rare, locally aggressive spindle cellSpindle cellneoplasmNeoplasm that accounts for less than 1% of all soft tissue sarcomas and less than 0.1% of all malignancies. Immunohistochemical and ultrastructural studies indicate that the tumor is of fibroblastic origin. DFSP commonly occurs in the dermis and has the potential to invade fascial planes into the muscle and bone. It may occur in any part of the body, with a predilection for the trunk. There are several less common subtypes of DFSP, including myxoid, BednarBednar (pigmented), myoidMyoid, granular cell, sclerosing, atrophic, fibrosarcomatousFibrosarcomatous (DFSP-FS), and palisading/Verocay body prominent. The tumor rarely exhibits metastasis, but has a propensity for subclinical involvement. Complete surgical excisionSurgical excision is the mainstay of therapy. DFSP can be resected using either Mohs micrographic surgeryMohs micrographic surgery (MMS) or wide local excisionWide local excision (WLE). The exact role of neoadjuvant radiotherapyRadiotherapy and imatinib mesylateImatinib mesylate in DFSP management remains unclear. Successful treatmentTreatment outcomes depend on achieving negative surgical margins, while preventing functional deficits.