Uveal melanocytes are derived from neural crest and share this embryologic origin with cutaneous melanocytes. The spectrum of observed variants of choroidal melanocytic lesions can be explained on the basis of embryogenesis and migration of uveal melanocytes. Benign melanocytic uveal tumors are generally known as nevi (also spelt as “naevi”). Nevus is a Latin word meaning birthmark or mole and is a general term for a congenital mark on the skin. In ophthalmology, the term nevus refers to an abnormal, hamartomatous cluster of melanocytes. This chapter describes choroidal and ciliary body nevi as well as oculo(dermal) melanocytosis and melanocytoma, which are considered as variants of nevus.