Stridor, a high-pitched, harsh respiratory noise, results from turbulent airflow through a restricted air passage, commonly observed during inhalation. It is more prevalent in pediatric cases than in adults. Notably, stridor is not a standalone diagnosis; rather, it serves as a key indicator of an underlying condition, which can vary from a chronic symptom present at birth or shortly after to an acute presentation at any age. Stridor can be attributed to both congenital malformations and acquired factors. Congenital stridor is commonly associated with conditions such as laryngomalacia, vocal cord paresis, subglottic stenosis, vascular ring, or glottic web. Conversely, acquired stridor may result from conditions like croup, epiglottitis, bacterial tracheitis, retropharyngeal abscess, or foreign body aspiration. The epidemiology of stridor relies on the specific underlying cause. The severity and origin of the stridor dictate the signs of respiratory distress, including dyspnea, nasal flaring, intercostal or subcostal retractions, grunting, cyanosis, somnolence, and periods of apnea. To establish a diagnosis, a comprehensive approach is necessary, involving a detailed history, thorough physical examination, and flexible fiber-optic endoscopy. In some cases, further evaluation with direct laryngoscopy and bronchoscopy under general anesthesia may be required. Management focuses on treating the underlying pathology responsible for the stridor.