Superior Canal Dehiscence Syndrome

Numerous auditory and/or vestibular signs and symptoms may be present in patients with superior canal dehiscence syndrome (SCDS). The superior semicircular canal (SSC) has a thinning or nonexistent bone cover, which is linked to these symptoms. There may be signs of autophony, oscillopsia, pulsatile tinnitus, pressure- and sound-induced vertigo, and hyperacusis (bone conduction). Lower-than-normal bone conduction thresholds on pure-tone audiometry (PTA) and particular findings on ocular and cervical vestibular-evoked myogenic potential (cVEMP thresholds below normal and high oVEMP amplitude) are observed, along with nystagmus linked to inhibition or stimulation of the afflicted SSC. In order to diagnose SCDS, high-resolution computed tomography (CT) scanning is also essential. Regarding the surgical strategy, repair techniques, and therapeutic materials, there is no agreement in the literature. In light of the literature, this chapter provides a detailed discussion of SCDS.