Correction of Tibia Recurvatum and Shortening in Skeletal Dysplasia

A 14 year old male presented with an unknown presumed autosomal dominant skeletal dysplasiadysplasia with proximal tibia recurvatumrecurvatum and leg length discrepancyleg length discrepancy. He also had asymptomatic platyspondyly and mild scoliosis once his pelvis was balanced. His mother had the same phenotype. He had a severe limp with a back knee and short leg gait. He was treated with a proximal tibia-fibula osteotomy, application of a circular external fixatorcircular external fixator with gradual correction of the recurvatum and lengthening of the tibia until the pelvis was balanced and the knee had satisfactory motion. After satisfactory consolidation, the frame was removed with excellent clinical and radiographic outcome. This method was chosen to avoid complications of an acute osteotomy such as knee stiffness, neurovascular injury/compartment syndrome, or inadequate correction.