Eleven Year Old Child with Osteogenesis Imperfecta Type III and Multiple Severe Deformities, Treated with Telescoping Fassier-Duval Rods

An 11 year old boy with osteogenesis imperfecta type III presented to our clinic with multiple lower limb deformities. He was on bisphosphonate treatment and had no previous surgeries. He was wheelchair bound because of the severe deformities and previous multiple fractures. He successfully underwent femoral and tibial rodding on one side with telescoping Fassier-Duval rods, followed by the other side 3 weeks later. He was immobilized in a posterior slab for 3 weeks and then for another 3 weeks in long leg braces for a total 6 weeks non-weight bearing. Partial weight bearing with intense physiotherapy was then started. At 3 months postoperatively he was able to walk independently with long leg braces and a walker. Two years postoperatively, the osteotomies were healed and the rods were telescoping. Since then, he has been ambulating independently with braces and a walker.