Cubitus Varus Deformity due to Multiple Hereditary Exostosis Treated with Ulnar Lengthening and Closed Radio-Capitulum Reduction

A 7 year old boy with multiple hereditary exostoses presented with progressive swelling of the left elbow and reduced range of elbow motion. Radiographs showed a distal ulnar exostosis, ulnar negative wristUlnar negative wrist, and subluxation of the radiocapitellar joint. On follow-up, the elbow deformity became worse. Repeated radiograph showed lateral dislocation of the radiocapitellar joint (Masada type IIB). He was treated with gradual lengthening of the ulnar and distal distraction of radius using an Ilizarov external fixator. The radiocapitellar joint was gradually reduced during the ulnar lengthening. Following the removal of the Ilizarov external fixator, the radial variant was also corrected with proximal migration of the radius. General appearance of the elbow improved with a slight increase in elbow flexion. On the last follow-up, a similar deformity was noted to be developing in the opposite elbow.