Correction of Forearm Deformities in Herediatry Multiple Exostosis (MHE)
摘要
Hereditary multiple exostoses (HME) may cause significant upper limb deformities and disabilities. Forearm deformities are the most common manifestation of this syndrome in the upper limb. The underlying cause is disturbance of growth of the distal ulna, leading to shortening of the ulna, and subsequent tethering of the radius with resultant ulnar deviation of the distal radius. In this case presentation, acute correction of the radial deformity with acute Z-lengthening of the ulna fixed both deformities simultaneously and without the need for external fixation.