Complete Atrioventricular Septal Defect

The complete atrioventricular septal defect (AVSDAtrioventricular septal defect (AVSD)) is a variant of AVSDAtrioventricular septal defect (AVSD) with significant atrial and ventricular components and a common atrioventricular valveCommon atrioventricular valve (AVV). A high proportion of cases are detected prenatally. It is often associated with Trisomy 21 (Down syndrome). The patients usually develop symptoms of heart failureHeart failure early in life. All patients with complete AVSDAtrioventricular septal defect (AVSD) require surgical intervention, usually at 3–6 months of life, with low morbidity and mortality. Late referrals are at high risk of pulmonary vascular diseasePulmonary vascular disease, especially if Trisomy 21. Complex forms of AVSDAtrioventricular septal defect (AVSD) include associations with Tetralogy of FallotTetralogy of Fallot (TOF) and atrial isomerismIsomerism. Main indications for reoperation are left atrioventricular valveLeft/right atrioventricular valve regurgitation, left ventricular outflow tract obstructionLeft ventricular outflow tract obstruction, or residual shunt.