Pulmonary Hypertension

Pulmonary arterial hypertension (PAH) in childrenChildren carries a poor prognosis. There are multifactorial elements in pediatricPediatric pulmonary hypertensive vascular disease, including lung developmental abnormalities, geneticGenetics associations, pathological insults on a growing lung as well as other diseases and conditions. This chapter will focus on the most common presentations of pulmonary hypertensionPulmonary hypertension (PH) in childrenChildren. The etiologic variety, clinical presentation and differences in outcomes require a unique, multidisciplinary approach to management.