Choroid Plexus Tumors

Choroid plexus tumors (CPT) are rare tumors of the neuroepithelial tissue of the brain that are most common in young children. They account for <1% of all intracranial tumors. In adults, they arise most frequently in the fourth ventricle, often presenting with hydrocephalus due to overproduction of cerebrospinal fluid (CSF). There are three histopathological classifications of choroid plexus tumors: choroid plexus papilloma (CPP), atypical choroid plexus papilloma (ACP), and choroid plexus carcinoma (CPC). Histology and extent of surgical resection are prognostic for choroid plexus tumors. Curative treatment for CPP and ACP is typically maximum surgical resection, although recurrence rates are higher in cases of ACP. CPP and ACP have better prognosis than CPC, which often requires multiple modalities for treatment.