Hypertrophic Cardiomyopathy in Children

Hypertrophic cardiomyopathy (HCM) is a rare condition in infants and children. HCM is a genetic disorder affecting the heart alone or in combination with other organ disorders. HCM has a diverse set of genetic causes and clinical manifestations. The most significant concern in HCM is the risk of sudden cardiac death. In this chapter we review terminology and nomenclature associated with HCM, etiological factors, types of HCM, diagnostic tools used to diagnose and evaluate HCM, and management of the various types of HCM.