Tricuspid Atresia
摘要
Tricuspid atresia is a rare congenital heart disease; however, a common defect in the subset of univentricular heart lesions. The absence of communication between the right atrium and ventricle due to tricuspid valve atresia results in a functionally univentricular heart necessitating palliative procedures, performed in a stepwise fashion towards a Fontan circulation. This chapter reviews the incidence, pathology, natural history, genetics, presentation, diagnosis, and management, both medical and surgical, of this congenital heart disease.