Congenital Mitral Valve Abnormalities

Congenital mitral valve abnormalities are a group of diverse defects that can result in varied clinical presentations depending not only on valvular function but also on the presence of associated congenital heart defects. This chapter reviews congenital abnormalities of the mitral valve leading to stenosis and/or regurgitation including: supravalvar mitral ring, isolated cleft mitral valve, double orifice mitral valve, the spectrum of mitral valve dysplasia (and mitral arcade), parachute mitral valve, Ebstein malformation of mitral valve, and mitral valve prolapse.