Background <p>A late-presenting total anomalous pulmonary venous connection is extremely rare, and surgical repair remains a significant challenge.</p> Cases presentation <p>We present two cases of surgical repair for late-presenting supracardiac total anomalous pulmonary vein connection: a 14-year-old female and a 32-year-old female. Both were successfully operated on and were discharged on postoperative days 9 and 29. The second patient had a prolonged hospital stay due to complications of acute kidney injury after surgery and the need for hemodialysis. Both patients had a small left ventricle and pulmonary hypertension preoperatively. All pulmonary veins drained to a common pulmonary vein, which drained to a left-sided vertical vein, which drained into the innominate vein. Postoperative evaluation of both patients found no pulmonary vein obstruction and good biventricular contraction.</p> Conclusion <p>Late diagnosis may occur in TAPVC patients, but a surgical repair may still be possible.</p>

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Surgical repair of extremely late presentation of supracardiac total anomalous pulmonary vein connection: a case series

  • Dicky Fakhri,
  • Salomo Purba,
  • Indriwanto Sakdijan,
  • Ardiansyah,
  • Aditya Agam Nugraha

摘要

Background

A late-presenting total anomalous pulmonary venous connection is extremely rare, and surgical repair remains a significant challenge.

Cases presentation

We present two cases of surgical repair for late-presenting supracardiac total anomalous pulmonary vein connection: a 14-year-old female and a 32-year-old female. Both were successfully operated on and were discharged on postoperative days 9 and 29. The second patient had a prolonged hospital stay due to complications of acute kidney injury after surgery and the need for hemodialysis. Both patients had a small left ventricle and pulmonary hypertension preoperatively. All pulmonary veins drained to a common pulmonary vein, which drained to a left-sided vertical vein, which drained into the innominate vein. Postoperative evaluation of both patients found no pulmonary vein obstruction and good biventricular contraction.

Conclusion

Late diagnosis may occur in TAPVC patients, but a surgical repair may still be possible.