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Background <p>Hutchinson-Gilford progeria syndrome (HGPS) is a rare genetic disorder that manifests itself in premature aging. Craniofacial and skeletal abnormalities, cardiovascular pathology, concomitant cerebrovascular diseases, and potential airway problems in HGPS significantly increase the degree of anesthetic risk and make anesthetic management more challenging in these patients.</p> Case presentation <p>We present the case of the girl with HGPS who undertook two episodes of dental treatment using general anesthesia at the ages of 8 and 10 years old. In both cases, airway was secured by fiberoptic intubation.</p> Conclusion <p>This case increases the awareness of HGPS and the features of anesthesia in patients with HGPS. For long-term dental treatment, general anesthesia with tracheal intubation using fiberoptic access is the optimal method of anesthesia in these patients.</p>

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General anesthesia in patient with Hutchinson-Gilford Progeria syndrome: two case reports of dental treatment in the one patient

  • 期刊论文

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  • 发表日期：

    2026年2月17日

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  • B. Mankovsky,
  • O. Halushko,
  • Y. Zablotskyy,
  • M. Synytsyn

摘要

Background

Hutchinson-Gilford progeria syndrome (HGPS) is a rare genetic disorder that manifests itself in premature aging. Craniofacial and skeletal abnormalities, cardiovascular pathology, concomitant cerebrovascular diseases, and potential airway problems in HGPS significantly increase the degree of anesthetic risk and make anesthetic management more challenging in these patients.

Case presentation

We present the case of the girl with HGPS who undertook two episodes of dental treatment using general anesthesia at the ages of 8 and 10 years old. In both cases, airway was secured by fiberoptic intubation.

Conclusion

This case increases the awareness of HGPS and the features of anesthesia in patients with HGPS. For long-term dental treatment, general anesthesia with tracheal intubation using fiberoptic access is the optimal method of anesthesia in these patients.