Aim <p>Retrocaval ureter is a rare congenital vascular anomaly seldom encountered in the paediatric population. We aimed to evaluate our experience with retroperitoneoscopic surgical correction with ureteroureterostomy.</p> Method <p>We identified patients with retrocaval ureter following a search of our operative database and conducted a case note review to clarify whether a minimally invasive approach to ureteroureterostomy was effective and resulted in symptom improvement.</p> Results <p>Two patients underwent operative intervention for retrocaval ureter. Both patients presented with obstructive symptoms and unilateral hydronephrosis on radiological investigations. Patient A, a fit and well male with no past medical history. Patient B, a female with complex surgical history including complicated cloacal anomaly, VACTERL association, end colostomy, vaginal replacement and umbilical appendicovesicostomy with marked lumbar scoliosis to the right side. Median age at time of operation was 14years (range 13-15years) and mean weight was 51kg (range 41-61kg). Both patients underwent standard retroperitoneoscopic ureteroureterostomy with a mean operative time of 217.5minutes (range 215-225mins). Both patients were discharged on the second post-operative day. Mean duration of JJ stent placement was 78days (23-132days). Both patients experienced full symptom resolution.</p> Conclusion <p>Minimally invasive ureteroureterostomy is a viable operative strategy for retrocaval ureter. Retroperitoneoscopic approach is particularly advantageous in patients for whom a transperitoneal approach is not suitable and can be performed safely and effectively even when there is limited space as in our case with marked scoliosis.</p>