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<p>Biliary atresia (BA) is a progressive obliterative cholangiopathy causing obstructive jaundice. Rare variants like BASM syndrome and cystic BA present unique diagnostic challenges. We report two such cases where laparoscopy proved valuable for confirming diagnosis, assessing liver status, performing laparoscopic cholangiogram (LC), and enabling definitive surgical management in the same sitting. Laparoscopy could be of immense help in the diagnosis of biliary atresia, especially in rare variants, being minimally invasive as compared to a conventional intraoperative cholangiogram, and it also allows us to take a liver biopsy under vision, which makes it a valuable addition to the armamentarium of investigations for Biliary Atresia. Through an English language literature review, we would also like to hypothesize a subgroup of syndromic biliary atresia under a new heading of ‘Biliary Atresia and other Visceral Malformation (BAVM) syndrome’. We would intend to place syndromic Biliary atresias other than BASM syndrome under BAVM syndrome and unravel some insights regarding this new subgroup.</p>

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Beyond the ordinary: ancillary role of laparoscopy in diagnosing rare biliary atresia variants—our experience and insights

  • 期刊论文

  • 发表日期：

    2025年10月10日

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  • Aditya J. Baindur,
  • Shalvika Kashyap,
  • Praveen Mathur,
  • Ramesh Chand Tanger,
  • Anu Bhandari,
  • Priyanka Mittal,
  • Neelam Dogra,
  • Priti Vijay,
  • B. S. Nagashri

摘要

Biliary atresia (BA) is a progressive obliterative cholangiopathy causing obstructive jaundice. Rare variants like BASM syndrome and cystic BA present unique diagnostic challenges. We report two such cases where laparoscopy proved valuable for confirming diagnosis, assessing liver status, performing laparoscopic cholangiogram (LC), and enabling definitive surgical management in the same sitting. Laparoscopy could be of immense help in the diagnosis of biliary atresia, especially in rare variants, being minimally invasive as compared to a conventional intraoperative cholangiogram, and it also allows us to take a liver biopsy under vision, which makes it a valuable addition to the armamentarium of investigations for Biliary Atresia. Through an English language literature review, we would also like to hypothesize a subgroup of syndromic biliary atresia under a new heading of ‘Biliary Atresia and other Visceral Malformation (BAVM) syndrome’. We would intend to place syndromic Biliary atresias other than BASM syndrome under BAVM syndrome and unravel some insights regarding this new subgroup.