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Purpose <p>We report our experience with the clinical management of complex lung malformations: multilobar, multiple unilobar, and bilateral congenital lung malformations (CLM) associated with duplication cysts (bronchogenic or foregut) or congenital diaphragmatic defects including congenital diaphragmatic hernia (CDH) or diaphragmatic duplication (DD).</p> Materials and methods <p>This is a retrospective case notes review of all patients with complex lung malformations presenting to a tertiary center between 1997 and 2023. Patient demographics, pre-operative symptoms, antenatal and postnatal investigations, surgical intervention, and overall outcome were audited and reported.</p> Results <p>Twenty-four patients had complex lung malformations. Antenatally, 11 were diagnosed appropriately, while 13 were thought to have only a single malformation. Postnatal management identified a total of 53 abnormalities. Twenty-three patients underwent resection of 44 lesions (and 3 CDH repairs), demonstrating 10 histologically distinct lung malformations. Twenty patients underwent single-stage surgical management. Thoracoscopic lung parenchyma-sparing segmental CLM resection was achieved in 17 patients. There were no major complications. The average length of stay was 5&#xa0;days (range 3–14). No patients required readmission by day 30.</p> Conclusion <p>We recommend awareness of the coexistence of complex CLM and peri-diaphragmatic malformations. Minimally invasive, single-stage resection with lung parenchyma sparing is safe and produces very good outcomes.</p>

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Management of complex congenital lung malformations: multiple unilobar, bilobar or bilateral lesions or associated with other congenital peri-diaphragmatic malformations. Experience from a single center

  • 期刊论文

  • 发表日期：

    2025年4月9日

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  • Ashitha K. Unny,
  • Giampiero Soccorso,
  • Michael Singh,
  • Dakshesh Parikh

摘要

Purpose

We report our experience with the clinical management of complex lung malformations: multilobar, multiple unilobar, and bilateral congenital lung malformations (CLM) associated with duplication cysts (bronchogenic or foregut) or congenital diaphragmatic defects including congenital diaphragmatic hernia (CDH) or diaphragmatic duplication (DD).

Materials and methods

This is a retrospective case notes review of all patients with complex lung malformations presenting to a tertiary center between 1997 and 2023. Patient demographics, pre-operative symptoms, antenatal and postnatal investigations, surgical intervention, and overall outcome were audited and reported.

Results

Twenty-four patients had complex lung malformations. Antenatally, 11 were diagnosed appropriately, while 13 were thought to have only a single malformation. Postnatal management identified a total of 53 abnormalities. Twenty-three patients underwent resection of 44 lesions (and 3 CDH repairs), demonstrating 10 histologically distinct lung malformations. Twenty patients underwent single-stage surgical management. Thoracoscopic lung parenchyma-sparing segmental CLM resection was achieved in 17 patients. There were no major complications. The average length of stay was 5 days (range 3–14). No patients required readmission by day 30.

Conclusion

We recommend awareness of the coexistence of complex CLM and peri-diaphragmatic malformations. Minimally invasive, single-stage resection with lung parenchyma sparing is safe and produces very good outcomes.