Adipositas beim Prader-Willi-Syndrom (PWS)
摘要
Prader-Willi Syndrome is a genetically inherited condition in which a pathognomonic hyperphagia leads to obesity in almost all patients. Since obesity, with its comorbidities, is the main cause of death, treatment plays an important role. Medications have shown only moderate success in terms of Body Mass Index so far, but they can positively influence hyperphagia. Nutrition is the most important task in therapy management. It is important to consider the composition of meals and to implement age-appropriate behavioral measures. Despite new medications, obesity prevention remains the most important pillar for reducing morbidity and mortality.