Congenital Nasal Pyriform Aperture Stenosis Review of Literature, Single-Center Recommendation, and Case Study

Congenital nasal pyriform aperture stenosis (CNPAS) is a rare disorder that causes airway obstruction in newborns and children. Patients with CNPAS mainly present with nasal obstruction, respiratory distress, feeding difficulties, and/or failure to thrive. Here, we present the case of a 1-day old male baby born with tachypnea, nasal obstruction, and congestion. Clinical examination revealed subcostal retraction and nasal obstruction. Nasal examination revealed an inability to pass the neonatal scope bilaterally and narrowing of the nostrils. Imaging revealed an isolated narrowed pyriform aperture of 4.5 mm. The patient was treated conservatively, and he showed significant improvement.