Successful ventricular septation and mitral valve repair in an 18-month-old with a single ventricle anatomy
摘要
Single ventricle anatomy, with two atrioventricular valves opening into two ventricles but with a large portion of the septum missing, is typically managed via staged single ventricle palliation. We present a case where ventricular septation and mitral valve repair were successfully achieved. A 3-month-old infant presented with cachexia and pneumonia. Echocardiography revealed a large ventricular septal defect (VSD) occupying most of the septum. The right ventricle (RV) was bipartite. Severe mitral regurgitation developed post pulmonary artery (PA) banding. After careful assessment and consideration, at 18 months of age, the patient underwent successful mitral valve repair, ventricular septation, and PA debanding. This case highlights the potential for achieving biventricular repair in select patients with single ventricle anatomy.