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Background <p>According to the International Society for the Study of Vascular Anomalies (ISSVA) 2025 classification Fibroadipose vascular anomaly (FAVA) is a slow-flow venous malformation and can lead to painful lesions in the muscles of the extremities in children and young adults with considerable restriction of movement and even pronounced contractures.</p> Objectives <p>The aim of the article is to present the experiences with this clinical picture based on a&#xa0;series of patients treated in our clinics and to summarize the diagnostic criteria and treatment approaches based on the current literature.</p> Material and methods <p>All patients diagnosed with FAVA and treated at the Department of Vascular Surgery at the Munich Clinic Bogenhausen and the Department of Pediatric Surgery at the Munich Clinic Schwabing from 2016–2023 were retrospectively interviewed about preoperative symptoms, postoperative well-being and quality of life.</p> Results <p>A&#xa0;total of 9&#xa0;patients presented to our clinics with a&#xa0;suspected diagnosis of FAVA. In 8&#xa0;patients this diagnosis was histologically confirmed postoperatively, 7 of the 9&#xa0;patients reported a&#xa0;significant improvement in symptoms after surgical resection and 2&#xa0;patients had to be operated on again.</p> Conclusion <p>The FAVA is a&#xa0;rare vascular malformation but due to the special treatment approaches it is nevertheless important to recognize it early and to differentiate it from other vascular malformations. Early treatment is essential to avoid functional limitations.</p>

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Diagnostik und Therapie der fibroadipösen vaskulären Anomalie (FAVA)

  • 期刊论文

  • 出版模式：

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  • 发表日期：

    2025年11月18日

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  • Ekaterina Nedeoglo,
  • Andreas Saleh,
  • Hubert Stiegler,
  • Andreas Maier-Hasselmann

摘要

Background

According to the International Society for the Study of Vascular Anomalies (ISSVA) 2025 classification Fibroadipose vascular anomaly (FAVA) is a slow-flow venous malformation and can lead to painful lesions in the muscles of the extremities in children and young adults with considerable restriction of movement and even pronounced contractures.

Objectives

The aim of the article is to present the experiences with this clinical picture based on a series of patients treated in our clinics and to summarize the diagnostic criteria and treatment approaches based on the current literature.

Material and methods

All patients diagnosed with FAVA and treated at the Department of Vascular Surgery at the Munich Clinic Bogenhausen and the Department of Pediatric Surgery at the Munich Clinic Schwabing from 2016–2023 were retrospectively interviewed about preoperative symptoms, postoperative well-being and quality of life.

Results

A total of 9 patients presented to our clinics with a suspected diagnosis of FAVA. In 8 patients this diagnosis was histologically confirmed postoperatively, 7 of the 9 patients reported a significant improvement in symptoms after surgical resection and 2 patients had to be operated on again.

Conclusion

The FAVA is a rare vascular malformation but due to the special treatment approaches it is nevertheless important to recognize it early and to differentiate it from other vascular malformations. Early treatment is essential to avoid functional limitations.